What is vulgar ichthyosis

Content

  • Vulgar ichthyosis
  • Diagnosis of vulgarngo ichthyosis


  • Vulgar ichthyosis

    Vulgar ichthyosis (Ichthyosis vulgaris) - disease inherit
    Autosomal dominant with high penetrance (The frequency with which this feature is controlled by one or another genome) Gena. Initial signs
    Diseases are detected in the first months of the child's life. Maximum
    development process reaches 10 years and continues all
    Life with improvements in the summer and during puberty.
    Disease may proceed with different intensity. Disease
    common, characterized by dry, thickening of the skin, but without inflammatory changes, without
    Erythema (strong leather redness). Especially expressed dryness and peeling on extensitive
    The surfaces of the limbs in the area of ​​elbow and knee joints. Leather
    axillary, elbow, popliteam, crotch, palms and soles
    Not changed. In children up to 4-5 years, the skin is involved in the process. IN
    Lobal and cheek areas can see lamellar or seven
    Chesows grayish-dirty color.

    Depending on the color of scales, their appearance, severity
    dry skin distinguish several clinical varieties of vulgar
    ichthyosis.

    What is vulgar ichthyosisKerodermia (Xerodermia) - initial, easiest
    A variety of ichthyosis at which skin dryness is observed, peeling
    Buddly, mainly on the front surfaces
    upper and lower extremities and partly on the skin of the body.

    Simple ichthyosis (Ichthyosis Simplex) - Second more
    Intensively pronounced variety. Dry skin expressed
    more considerable, there is a rich number of lamellar scales, tight
    adjacent to thickened, dry, rigid and rough skin.

    Brilliant ichthyosis (Ichthyosis Nitida) Manifests (manifests)
    significant accumulation of horny scales, distinguished by pearl
    shine or having a slightly brilliant, as if lacquered, surface.
    In the presence of whiskers of pearl scraps, they use the term «White
    ichthyosis». Sometimes scales become thicker, more densely, acquire
    Dark gray color and lingering linen, tightly adjacent to the skin
    and distinguishing deep furrows. Such a clinical form
    ichthyosis is called snake-shaped (Ichthyosis Serpentina). The hardest
    A variety is a cylinder ichthyosis (Ichthyosis Hystrix), with
    which clusters are located on the front surfaces of the limbs
    thick horny masses in the form of spikes protruding on 1 - 10 mm above
    The surface of the skin resembling the needles of the dickery.

    Hair and nails with light formations of ichthyosis are not changed and general
    The patient's condition remains quite satisfactory. However, children with
    Heavy forms of ichthyosis Hair Dry, thinned, rarefied.
    There are various onsidstrophy. Patients with ichthyosis due to
    Reduced Potion and Salo Distribution and Temperature Management
    Asthenized, lagging behind in physical and intellectual development. They have
    Immunodeficiency states, developmental tendency
    Piedlemiths, pneumonia, otites, eczema, neurodermit,
    Psoriasis. Imbecillopathy and disadvantages of the formation of phenotype are characteristic
    Children with severe forms of ichthyosis.



    Diagnosis of vulgarngo ichthyosis

    Clinical and morphological manifestations of all varieties
    vulgar ichthyosis differ in constancy. All forms of the disease
    occur in childhood. Therefore, the diagnosis of the process is not
    Represents difficulties. Differential diagnosis with acquired
    ichthyosis is based on available ichthiosis
    Avitamin Solid State, especially Vitamin A deficiency, blood disease
    Type of leukemia or lymphogranulation.

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