As this disease is manifested, and in what way is the diagnosis of idiopathic dermatomyomyosis? Juvenile dermatomyosis: its main symptoms and characteristic features.
Content
Systemic dermatomyosis — The disease is quite rare. The history of dermatomyositis disease reveals a direct connection with inflammatory-degenerative processes on the skin, disruption of motor functions, disease of the connecting and muscle tissue. However, the defeat of the muscles is the leading sign. Juvenile and Female Dermatomiomy — The most common forms of illness. Definite answer to the question: «What is the cause of this disease?» Today there is no. The subject of studying medical science is still the skin and muscle system of the body.
In adults, the disease most often occurs after a long insolation, actions of some vaccines, viruses and various infectious diseases. Sometimes bacterial pathogens may also cause illness. In addition, the history of illness «Dermatomiosit» Often conjugate with genetic factors and hereditary predisposition.
The classification of idiopathic dermatomyositis divides the disease by origin and by its flow.
Basic signs of system dermatomyositis
The main symptoms and signs of the disease with the general dermatomyositis are the defeat of large joints and skeletal muscles, heart and lungs, gastrointestinal tract and endocrine system. In the acute period, the history of the disease is manifested by noving pain in the muscles of the hands, feet and torso, which are enhanced with significant physical activity. Stiffness in motion with an extensive briefing of the connective tissue is a sign of a durable process
A characteristic symptom of the disease is the appearance of erythema — Skin redness «Points», Located on zoom bones, wings of nose and nasolabial fold. Rashes are celebrated in the field of the upper departments of the chest, back, elbow, knee and interphalating joints.
Dermatomyomy in children
In most cases, the disease develops as an idiopathic process, usually occurs after vaccinations and is most dangerous among other systemic diseases.
A feature of this disease is the weakening of the functional activity of the germ. Usually, hypothalamus and adrenal bark are involved in the pathological process.
Clinical manifestations of idiopathic or primary dermatomyositis
A characteristic feature of the disease is calcium of soft tissues, which is based on the deposition of calcium salts in the muscles, which dramatically limits the patient's motor activity. This feature is often found at juvenile form, less — in adults.
When involving the muscles of the muscles, larynx in the process of muscle disease, the esophagus is broken, difficulties appear when swallowing and coughing attacks arise. With a long-term course of the disease, there is a swelling and painfulness of muscles, and in some cases — Muscular atrophy.
In the case of damage to intercostal muscles and muscles of the diaphragm, the occurrence of pulmonary and respiratory failure. Reduced ventilation function of lungs and symptoms of interstitial pneumonia — These are clinical manifestations of the history of the system of system classic deratomositis.
General signs of the disease are manifested by the defeat of the shells of the heart, myocardium, heart rate impaired, increased liver with a violation of its functional activity, abdominal pain, malaise, fever and decrease in appetite.
Diagnosis of the disease
The basis for the diagnosis of the disease is to carry out histological research and analyzes of blood both in common and biochemical. At the same time, the growth of ESP, leukocytosis, increased hepatic enzymes and change in the level of uric acid.
When forming a differential diagnosis should be held parallels with such diseases as systemic sclerodermia, photodermatosis, nodular periaryitis, exudative erythema, red lupus.
The diagnosis of the disease is reliable only when there are 2-3 signs described above, and especially typical for this disease — Skin and Muscular Syndrome.
