What caused hypervalinemia disease? What are the symptoms of this disease? How to treat him? Read in this article.
Content
Causes
Hereditary disease due to deficiency of valintransferase with an increase in breeding concentration in blood and urine;
Manifestations of hypervalinemia
The largest toxic (poisoning) action is on the central nervous system, which is manifested in the form of vomiting, lethargy, muscular twitching, nystagma (movements of eyeballs). The child lags behind in growth and weight, late begins to keep his head, sit. No treatment occurs a steady reduction in intelligence.
Treatment of hypervalinemia
The principle of treatment is that the dose of valine in food does not exceed 75—100 mg per 1 kg of body weight. Against the background of such treatment, vomiting quickly disappears, the child begins to add in weight and develop normally. Studies of the electrical activity of the brain in dynamics can serve as an effectiveness criterion for such a diet.
Content of valine in products (in grams per 100 g of product):
one. Women's milk — 0.072.
2. Milk cow — 0.189.
3. Kefir — 0.183.
4. Cottage cheese — 0,695.
five. Chicken egg — 0.895.
6. Meat beef — 1,156.
7. Chicken meat — 1.024.
eight. Beef liver — 0,987.
nine. Cod — 0.929.
10. Rice croups — 0.425.
eleven. Semolina — 0.386.
12. Buckwheat — 0.343.
13. Oatmeal cereals — 0.384.
fourteen. Croup-ray — 0.333.
fifteen. Pearl cereals — 0.313.
sixteen. Peas — 0.804.
17. Wheat flour — 0.387.
18. Pasta — 0,412.
nineteen. Rye bread — 0,062.
twenty. Wheat bread — 0.286.
21. Biscuit — 0.054.
22. Potato — 0,090.
23. Carrot — 0,053.
24. White cabbage — 0,053.
25. Tomatoes — 0.018.
26. Oranges — 0.013.
27. Lemons — 0,014.
28. Apple juice — 0.012.
29. Orange juice — 0.011.
thirty. Lemon juice — 0.016.
