Overview of pathology
Whatever incredible it seemed to, but the proprietary is really launched in the young organism premature aging mechanisms. Officially, the disease was named after scientists who first described and studied pathology: children are Hatchinson-Guilford syndrome, in adults - Werner syndrome.
Boys preteria is found several times more often than girls. On average, patients live from 10 to 13 years (in exceptional cases to 20): the fatal disease, unfortunately, does not give a chance to recovery and for many years of life. Such kids are noticeably lagging behind in physical development from healthy peers, but this is not all «Prelas» Spring. Strong exhaustion of the body, disrupting the structure of the skin, the lack of secondary signs of sexual development and hair, underdeveloped internal organs and the appearance of the old man as a whole - this is the cargo that falls on the shoulders of the unfortunate child.
In mental development, the child is absolutely adequate, his body retains children's proportions, but at the same time epiphyseal cartilage quickly overcomes and the epiphyseal line appears in its place - everything like an adult person. Rapid growing children are forced to face far away with children associated with a wheelchair: atherosclerosis, stroke, a variety of heart disease.
Causes of pathology
Immediately after the birth of children who carry a death gene of a wheelchair, not distinguish from healthy kids. Already by the first year of life, numerous symptoms of illness make themselves known to fully. Among them:
- Visible flaw in body weight, very small growth.
- Lack of hair on the head, eyelashes and eyebrows.
- The absence of subcutaneous fat and lack of tone in the skin - it is weak and wrinkled.
- Blue Skin Skin.
- Skin hyperpigmentation.
- Strongly protruding veins under the skin on the head.
- Disproportionate development of the bones of the face and skull, a small lower jaw, stacked eyes and outpopped ear shells, hooked nose - in a child «Bird» facial expression. It is this set of specific features makes it look like an old man.
- Later the appearance of teeth that quickly deteriorate.
- Voice - shrill and high.
- Pear-shaped chest, small clashes, «Tight» knee and elbow joints, which because of bad mobility forcing the patient to be in the pose «Rider».
- Yellow convex nails - «hour glass».
- SclerAnoise Education on the skin of the buttocks, hips and abdominal nose.
After a child suffering from a wheelchair, he will celebrate his fifth birthday, in his body starts inexorable development processes Atherosclerosis, at which the aorta, mesenteric and coronary arteries are particularly suffering. Against the background of these violations, the appearance of heart noise and left ventricular hypertrophy. The complex influence of these violations on the body is considered one of the reasons for the short life of patients with a wheelchair. The main factor in the supreme death of patients is called Myocardial infarction and ischemic stroke.
Sphere in adults
Adult person disease may unexpectedly overtake aged 14-15 to 18 years. The patient begins to lose weight, fall behind in growth, seen and gradually bald (progressive alopecia). The skin of the diseaseproof is thinned, loses all the paints, acquiring an unhealthy pale shade. Under it, the grid of blood vessels, subcutaneous fat and muscles are completely atrophy, so hands and legs seem very thin.
In patients who oversail a 30-year-old frontier, both Eye Apple amazed cataract, Wakes voice, leather over bone protrusions Grubets and covered with ulcers. Surprisingly perspective look like the same type: low growth, moon-shaped face, nose resembling bird beak, narrow mouth, sharply protruding chin, dense body and thin dry limbs, disfigured with numerous pigment stains. The disease unceremoniously interferes in a variety of organism systems: the work of sweat and sebaceous glands is disturbed, the normal activity of the cardiovascular system is distorted, the body suffers from calcification, osteoporosis and erosive osteoarthritis. In contrast to small patients, in adults, the disease adversely affects intellectual abilities.
About 10% of patients by forty years face such terrible diseases like Sarcoma, mammary cancer, Astrocitoma, Melanoma. Oncology develops against the background of diabetes and disturbed functions of parachitoid glands. The immediate cause of the death of patients with proges in most cases is malignant tumors and cardiovascular pathologies.
Diagnosis of the disease
External symptomatic manifestations of pathology are so bright and eloquent that the disease is diagnosed, relying on the data of the clinical picture.
Treatment of the disease
Our site is forced to admit that the panacea from the wheelchair, unfortunately, does not exist. All treatments that are used today are also not always effective. However, doctors make everything that depends on them. So, all patients are under regular medical supervision, because with the help of monitoring the state of the cardiovascular system, you can detect the development of complications of one or another «Heart» Diseases.
All methods of treatment are pursued by the only, but vital goal - «to freeze» Disease, do not allow her to aggravate and facilitate the patient's condition, how much the possibilities of modern medicine allow. What can help experts?
- Application of minimum doses Aspirin, which can protect a person from a possible heart attack or stroke.
- The use of other medicines that are prescribed individually, based on the state of each individual patient. For example, medications from the Statin Group reduce the elevated level of cholesterol in the blood, and the so-called anticoagulants block the formation of thrombus. Often use growth hormone, which «Building» height and weight.
- The use of physiotherapeutic procedures that are developing rush to hard joints, allowing a person to not lose activity. And what can be more important for small patients?
- Removal of dairy teeth. The specifics of the disease contributes to the early penetration of permanent teeth in children, while the milk is very quickly spoiled, so they need to be deleted in a timely manner.
Prevention of the disease at the moment has not yet been developed.
